KHA-CARI Autosomal Dominant Polycystic Kidney Disease Guideline: Management of Polycystic Liver Disease.

a. We recommend screening for polycystic liver disease in all patients diagnosed with autosomal dominant polycystic kidney disease using abdominal ultrasound (1C). b. We recommend that all female patients with autosomal dominant polycystic kidney disease and liver cysts undergo counseling regarding the risks of pregnancy and exogenous estrogen exposure in worsening liver cyst growth (1C). c. We recommend that females at risk of symptoms from hepatic cysts avoid estrogen supplements (1D). d. We recommend that a multidisciplinary team (hepatologist, hepatobiliary surgeon, interventional radiologist, and nephrologist) care for patients with severe polycystic liver disease associated with autosomal dominant polycystic kidney disease (1D).